Cystic Fibrosis

Cystic fibrosis is a complex, multisystem genetic disorder that primarily affects the respiratory and gastrointestinal systems and requires lifelong, intensive management beginning in early childhood. The disease is characterized by abnormal chloride transport leading to thick, viscous secretions that impair organ function and increase infection risk. Nurses play a critical role in early recognition, daily management, acute exacerbation care, and long-term family education. Advances in therapy have improved survival, but morbidity remains significant without consistent, evidence-based care. This course provides comprehensive, compliance-ready instruction focused on nursing responsibilities across settings.